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Primary lateral sclerosis
1 OMIM reference -
1 associated gene
3 connected diseases
No signs/symptoms info
Disease Type of connection
Amyotrophic lateral sclerosis
Charcot-Marie-Tooth disease type 4J
Yunis-Varon syndrome
Synonym(s):
- Adult-onset PLS
- Adult-onset primary lateral sclerosis
- PLS

Classification (Orphanet):
- Rare genetic disease
- Rare neurologic disease

Classification (ICD10):
- Diseases of the nervous system -

Epidemiological data:
Class of prevalence: 1-9 / 100 000
Average age onset: variable
Average age of death: normal
Type of inheritance: autosomal recessive
External references:
1 OMIM reference -
No MeSH references

Gene symbol UniProt reference OMIM reference
FIG4 Q92562609390
No signs/symptoms info available.